Coagulation disorders: The disease must live on someone else's blood

Not being able to live anemia from other people, not having a strong impact, not playing sports . need constant care and treatment when needed. These are the requirements for patients with coagulopathy.

Every year, the number of patients with coagulopathy is managed by the Central Children 's Hospital at about 100 cases. This is really a burden for every family if they do not treat them, they cannot live.

Fresh blood transfusion to live

Baby Do Thi Vang (Photo: VNN)

On the surface, with white skin, the plump, no one thought that Do Thi Vang, in Hau Loc and Thanh Hoa, had anemia. Just 15 years old, Vang had to transmit 20 liters of blood. Of course, this is not the final number because of the need to maintain life, Vang needs blood whenever necessary.

At 3 years old, she discovered on the girl the bruises but not hurt.

The family was not too surprised by Vang's brother who also had bruising in his hands and abdomen. Vang's brother was diagnosed with a disease that did not quantify Vitamin K (one of the diseases related to coagulopathy). A few years older, once, cycling wine has bladder bled to bleed to hospital.

The most miserable is that by the time of the daughter's puberty, every month, until the period of the period, blood cannot be held, Vang has to transfer up to 20 liters of blood.

Dr. Duong Ba Truc, Head of Clinical Hematology Department (National Hospital of Pediatrics) said: "For Baby Vang's case, we have to use non-hormonal drugs to appear to prolong the menstrual cycle. Fresh blood transfusion ''.

Bui Thi Thu, 3 months old, is in her mother's arms (Photo: VNN) Taking care of her daughter for nearly a month in the hospital, Ms. Nguyen Thi Tu, her mother Vang confided: "This is the third time I follow my son. go to the hospital. The whole family worked every time they took care of the hospital but they had to try. The longest period of treatment was in 2004 when the family borrowed borrowed money to meet the demand of treating children. The time to know the disease and how to treat it every few months also take several million ''.

Both brothers have a coagulopathy but are lucky to be discovered and treated promptly.

Meanwhile, a child of Ms. Bui Thi Quyen in Thai Nguyen died when she was just over 3 months old. Because the whole family thought she had dermatitis when the red spots appeared on her face.

Families who give babies to the provincial hospital are diagnosed with a fever and returned home for treatment. After that, she still cried and weakened, and the whole family went to the hospital for emergency treatment.

Drawing on the experience of his brother, Bui Thi Thu's daughter, only 3 months and 10 days, also had unusual signs: purple in her armpits, bleeding for 2 days without holding . Ms. Quyen took her to the Central Children's Hospital. Here, doctors diagnosed Thu's illness with a coagulopathy-related disease and must be treated with vitamin K.

Continuous care and treatment when needed

That is the requirement for those who unfortunately suffer from this disease. According to Dr. Duong Ba Truc, these patients suffer from Hemophilia.

This is a genetic coagulopathy caused by a decrease or abnormal clotting factor. Disease manifestations are long-lasting bleeding throughout parts of the body and most commonly in the muscles and joints.

Genetic diagram of coagulation disorder (Photo: VNN)

This is a genetic coagulopathy caused by a decrease or abnormal clotting factor. Disease manifestations are long-lasting bleeding throughout parts of the body and most commonly in the muscles and joints.

Dr. Duong Ba Truc said: There are many grassroots health facilities due to lack of coagulation tests, deep understanding of the disease, even ignorance of the disease, leading to patients suffering from complications due to misdiagnosis.

In addition to patients taking care of themselves, doctors also need to improve their understanding of the disease and its treatment.

This is a disease that requires lifelong treatment and is quite expensive and genetic.

Children with coagulopathy are prone to bruising .Hemophilia is usually only seen in men and cannot be cured.However, if given full care and preventive bleeding, patients can live almost normal people.

Hemophilia mild can only be detected when the patient reaches adulthood.But often symptoms appear right from a young age.Parents may find the child very easily bruised and prolonged bleeding when a small collision or cut.

The disease can be caused by genetic mutations, but most are inherited.The mother carries the hemophilia gene and is not sick, but transmits the gene to the sons.

Meanwhile, health insurance has not paid for cases of congenital and genetic diseases. Many families find it difficult to get sick. Therefore, health insurance coverage is essential.

"Now in advanced countries, biotechnology has been used to make it against hemophilia without the need for blood from other people. However, this is a new and expensive drug, so hospitals are now suggesting to import hemophilia but not being able to buy it on their own, 'said Dr. Truc.

In the immediate future, when there is no anti-hemophilia drug to maintain good life, people with this disease need the help of the community through the humanitarian blood donation program.

It is known that in Vietnam, it is estimated that there are about 5,000 patients with this disease in which the number diagnosed and managed is 800 (accounting for 16%). In particular, nearly half of hemophilia patients have a family history, in many cases a family with many sick people and a family with many sick lives.

In the opinion of experts, to limit the incidence, patients need to be detected early. For example, if you already have a hemophilia in your family, it is necessary to get genetic instructions from your doctor before deciding to give birth to your child.

Le Ha